DES
desmin
Synonyms:
CSM1, CSM2, LGMD2R
Species:
Human DES (1674), Mouse Des (13346), Rat Des (64362), sheep DES (101117308), Domestic Rabbit DES (100328890), domestic guinea pig Des (100733478), naked mole-rat Des (101716469), chicken DES (395906), cow DES (280765), domestic cat DES (101097010)
UniProtKB ID:
Gene ID:
- Human(1674) Summary: This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]
- Mouse(13346) desmin
- Rat(64362) desmin
- sheep(101117308) desmin
- Domestic Rabbit(100328890) desmin
- domestic guinea pig(100733478) desmin
- naked mole-rat(101716469) desmin
- chicken(395906) desmin
- cow(280765) desmin
- domestic cat(101097010) desmin
- dog(497091) desmin
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Antibodies
Product Number
Description
Species Reactivity
Application
Monoclonal Anti-DES antibody produced in mouse, Prestige Antibodies® Powered by Atlas Antibodies, clone CL4502, purified immunoglobulin,
Species Reactivity
human
Application
immunofluorescence
western blot
western blot
Monoclonal Anti-DES, (C-terminal) antibody produced in mouse, clone 1D12, purified immunoglobulin, buffered aqueous solution,
Species Reactivity
human
Application
ELISA
western blot
western blot
Anti-DES antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Species Reactivity
human
Application
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
Anti-DES antibody produced in rabbit, affinity isolated antibody,
Species Reactivity
bovine, dog, guinea pig, horse, human, mouse, rabbit, rat
Application
western blot
Anti-Desmin antibody produced in goat, ,
Species Reactivity
human, mouse, pig, rat
Application
ELISA
immunohistochemistry
western blot
immunohistochemistry
western blot